Exercise 1
For each pedigree, determine the most probable inheritance pattern,
assuming monogenic inheritance and full penetrance.
Pedigree 1
Pedigree 2
Pedigree 3
Pedigree 4
Pedigree 5
Exercise 2
A 25-year-old healthy woman seeks genetic counseling for a hereditary
skin condition, ichthyosis, which is present in her family. Ichthyosis
is characterized by dry, thickened, “fish-scale” skin.
- The woman has a younger brother and sister, both unaffected.
- Her father has ichthyosis.
- The father’s older brother is also affected, while their two older
sisters are healthy.
- The father’s affected brother has three healthy children: a
26-year-old son and two 22-year-old monozygotic twin daughters.
- The woman’s mother has a younger brother with intellectual
disability but no skin disease.
- The woman’s maternal and paternal grandparents are deceased and were
unaffected. However, the paternal grandmother had a brother with
ichthyosis.
- Draw the pedigree for this family.
- What is the most likely mode of inheritance for this disease?
Justify your answer.
- The woman begins a relationship with her father’s brother’s son. If
they have children, what is the probability that their child will
inherit ichthyosis? (Hint: Use a Punnett square to determine the
risk.)
Exercise 3
In the pedigree below, filled symbols represent individuals affected
by chronic granulomatous disease.
- Assuming the disease is X-linked recessive:
- Which individuals are obligate carriers of the disease-causing
allele?
- How should obligate carriers be indicated in the pedigree?
- What is the probability that individual II-4 is a carrier of the
disease-causing allele?
- What is the probability that individual III-1 will develop the
disease?
- Assuming the disease is autosomal recessive, and individual II-5 is
not a carrier:
- Which individuals are obligate carriers of the disease allele?
- What is the probability that individual II-4 is a carrier?
- What is the probability that individual III-1 has inherited the
disease-causing allele?
- Assuming the disease is autosomal recessive, with a population
disease frequency of 4 in 10,000:
- What is the probability that individual II-5 is a carrier?
- If you take the above risk into consideration, what is then the risk
that III-1 will get the disease?
Exercise 4
What is the genetic distance between locus \(A\) and \(B\) in the three examples below?
Exercise 5
The two genetic marker loci, \(A\)
and \(B\), are located on chromosome 9,
with a genetic distance of 15 cM between them.
- Marker locus A has two alleles, \(A_1\) and \(A_2\)
- Marker locus B has two alleles, \(B_1\) and \(B_2\)
The father is heterozygous at both loci, carrying the haplotypes
\(A_1B_1\) and \(A_2B_2\). The figure below illustrates
chromosome 9, depicting both loci and their respective alleles.
- Draw a similar chromosome set and position the father’s
alleles.
- Describe the different gametes that the father can produce and
account for the frequencies of these gametes.
Exercise 6
A monogenic hereditary disease is present in the pedigree shown
below. A marker locus located in the first intron of the disease gene
has two alleles, A and B. The genotypes for this marker locus are
provided for individuals II-2, III-2, and III-3 in the pedigree.
A. Based on the available genotype data, can we determine which
marker allele (A or B) is located at 0 cM distance to the disease
allele? Justify your answer. B. If we assume that II-1 has the genotype
BB, does this allow us to conclusively determine which marker allele is
linked to the disease allele? C. If the fetus IV-1 has inherited the
disease allele, what genotype is expected at the marker locus?
Exercise 7
Assume an X-linked recessive monogenic disorder with full
penetrance.
- Based on all the information in the pedigree below, what is the
probability that II.3 is a carrier of the monogenic disease-causing
allele? (Hint: Use Bayes theorem)
Exercise 8
Among Danish women with breast cancer, 3% carry a pathogenic variant.
Sanger sequencing detects pathogenic variants in BRCA1 and
BRCA2 with 80% sensitivity.
Lise, who is of Danish descent, underwent Sanger sequencing for
BRCA1 and BRCA2, and no pathogenic variant was
detected.
- What is the probability that Lise is still a carrier of a pathogenic
variant in BRCA1 and BRCA2 despite the negative test
result?